الفهرس | Only 14 pages are availabe for public view |
Abstract Heterotaxy syndrome is a general term that describes disruption in normal positioning of the visceral organs in the chest and abdomen.Heterotaxy syndrome, cardiosplenicsyndrome, right and left isomerism, and situs ambiguous are synonym for these defects. This study included 11 pediatric patients, their ages ranged from one day up to 18 months, most of cases (72.7%) below the age of 4 months, the main age is 3.44 months (103 days), they were 6females (two of them were sisters) and 5 males. The study was performedat Radiology Department, Mansoura University, from June 2013 till March 2016. The patients were referred from PediatricCardiology unit, Children’s Hospital, Mansoura University. The patients were suspected to have heterotaxy syndrome based on echocardiography findings. All cases under went CT with contrast on chest and upper abdomen (including non-ECG gating cardiac CTA) on either 128 or 16 MDCT scanners. The most common clinical presentation in our study was cyanosis; (6/11) of cases; five of these cases were diagnosed as right isomerism and the sixth case was diagnosed as situs inversus. In all thease cases pulmonary atresia and anomalous pulmonary venous return were detected. The other five cases presented with congestive heart failure symptoms; which includes tachypnea, interrupted feeding, poor feeding and tachycardia. All of these five cases were diagnosed as left isomerism. |